Hi All,

we have an infant with CCAM. Do You have any experiences with treatment of this disorder?

Thanx.

Most (all?) baies I've come across were managed conservatively.

Does the CCAM in your infant have any mass (compression) effects?

Yes, mediastinum is deviated towards the healthy (right) side, baby is still on vent, tomorow we will do scintigraphy of lungs and then we decide what we´ll be doing.

We had a baby about two months back.

He was a 34 week preterm baby, with massive CONG CAM of right lung with severe shift of mediatinum to the left. We had a hard time maintaining his oxygention. Within hours he was on very high pressures on conventional ventilator. Predictably developed bilateral pnemothoraces and had bilateral ICT in situ by the end of 3 hours of life.

But oxygenation was still a problem . We shifted him to HFOV and then used inhaled nitric oxide to try to balance V/Q matching.

That worked at dose of 40ppm. He stabilized. After few days he was "critically stable " enough to be operated and the lesion was excised by a lobectomy.

Following surgery he went to act very peculiarly after 2 weeks behaving like BPD. He again developed a left pnemothorax which ultimately resolved. He could not be weaned from ventilator support , and required unconventional institution of steroids as a last ditch effort. Now he is off steroids, recovering from fungal sepsis, on tube feeds. on low parameters on conventional ventilator. He is alert , looking around.

Both the baby and the doctor are waiting for the day he will be extubated.

He is now a 2 month old boy.

I will just update on the condition of the baby. He is now more than 5 months old. Now on oral feeding. Other than supplements , is not recieiving any medications. Is receiving supplemental oxygen 1 l/min. Is active and doing well.

Good to hear!

Happy to tell everyone, that the baby was discharged home last week. A very emotional moment for the parents and the NICU staff.

Baby had been weaned off oxygen for two weeks prior to discharge

Happy to tell everyone, that the baby was discharged home last week.

Great news! This is one of the nice aspects of neonatal care, happy endings!