What are the outcomes of congenital acinar dysplasia ( severe pulmonary hypoplasia ) in terms of resuscitation and mortality?

 

I have experienced this once (diagnosis from autopsy) when resuscitation failed completely.

There seems to be a few case reports published, like this one: https://onlinelibrary.wiley.com/doi/full/10.1111/jpc.13494_169

16 hours ago, Stefan Johansson said:

I have experienced this once (diagnosis from autopsy) when resuscitation failed completely.

There seems to be a few case reports published, like this one: https://onlinelibrary.wiley.com/doi/full/10.1111/jpc.13494_169

Thanks Stefan, your prompt reply is appreciated 

 

I have the experience of one case, which was published in 2003 ( Saudi Med J. 2003 Jan;24(1):88-90 ).

The diagnosis was done though lung biopsy. and the baby died at the age of around 2 months. The prognosis is very bad and the only management i the is lung-transplantation, which is difficult in this age.